Diagnostic Indications for Hepatic Transplantation in Children

Chronic cholestatic liver disease

Extrahepatic biliary atresia
Arteriohepatic dysplasia (Alagille syndrome)
Neonatal hepatitis
Primary sclerosing cholangitis
Caroli's disease
Lanerhan's cell histiocytosis (histiocytosis X)

Inborn errors of metabolism

Alpha-1-antitrypsin deficiency
Tyrosinemia
Wilson's disease

Miscellaneous metabolic or genetic liver disease

Glycogen storage disease, type 1
Glycogen storage disease, type 4
Type 1 hyperoxaluria
Crigler-Najjar syndrome
Ornithine transcarbamylase deficiency
Familial hypercholesterolemia
Protein C deficiency
Niemann-Pick and other lipidosis
Gaucher's disease
Erythropoietic protoporphyria
Hemophilia A
Hemophilia B
Urea cycle enzyme deficiency

Hepatocellular injury

Viral hepatitis
Autoimmune hepatitis
Drug-induced liver failure
Amanita mushroom poisoning

Mass occupying lesions

Hepatoblastoma
Hepatocellular carcinoma (hepatoma)
Polycystic liver disease
Hepatic adenomatosis
Hemangioendothelioma

Miscellaneous

Cystic fibrosis
Congenital hepatic fibrosis

 

 

Children’s Liver Association for Support Services
27023 McBean Parkway #126 Valencia, CA 91355
Toll-free: 1-877-679-8256 Local phone/fax: (661) 263-9099
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